Palabras clave: atrofia de múltiples sistemas (AMS), disautonomía, ataxia cerebelosa, el síndrome de Shy- Drager, la degeneración nigroestriada. (SND) y la. Shy-Drager syndrome a case report with polysomnography. Síndrome de Shy- Drager: registro de caso com estudo polissonográfico. F. S. Aloe; P.E. Marchiori; . A atrofia de múltiplos sistemas (AMS) é uma doença neurodegenerativa esporádica nigro-estriatal, atrofia olivopontocerebelar, síndrome de Shy- Drager.

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Sometimes it presents with low blood pressure on standing, urinary bladder problems, or difficulties with balance and movement that resemble Parkinson’s disease.

She presented progressive deterioration. J Neural Transm ; MRI of the brain showed the pontine “cross sign”, one draager feature of this type of disease Fig 1A.

Shy-Drager Syndrome: Causes, Symptoms, Treatment, Prognosis, Life Expectancy

Written, Edited or Reviewed By: Is It a Migraine? Pneumonia is the most common cause of death, although irregularities in heart beat or choking may be responsible for death in some patients. Sincrome therapy will be recommended for the patient to deal with dysphagia.

Evolution of sporadic olivopontocerebelar atrophy sindromd multiple system atrophy. Two years later autonomic dysfunction and pyramidal signs have appeared. Dietary increases of salt and fluid may be helpful.


Shy Drager Syndrome

The prognosis for Shy-Drager Syndrome is not that good as this condition is a disease process that progresses gradually with time. Report of two cases. Clin Auton Res ;8: All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License. Accepted 9 March What is Shy-Drager Syndrome? It is hard to establish the differential diagnosis with Parkinson’s disease, as it can be seen in our case.

HONselect – Shy-Drager Syndrome

Lippincott Willians and Wilkins, Shy-Drager Syndrome usually affects people who are above the age of 60 years. The possible mechanisms for this sleep disorder are discussed.

The cause is unknown. Ann Otol Laryngol These inclusions are constituted by alfa-synuclein, ubiquitin and tau protein 6,15, Services on Demand Journal. Oxford Univ Press, New York,pg Non-autonomic symptoms include Parkinsonism slowness of movement, stiffness of muscles, mild tremors, and loss of balancedifficulty moving eyes causing double vision and problems with focusing, problems controlling emotions and wasting of muscles. The patient may also undergo tests to look for any autonomic dysfunction like testing the bowel and bladder function of the patient, blood pressure monitoring, ophthalmologic examination to check the status of the eyes, EMG and nerve conduction studies to check the status of the functioning of the muscles and nerves.


The second case reports a patient presenting MSA-P or striatonigral degeneration and the brain MRI shows lenticular nucleus sign alteration. In Shy-Drager Syndrome, there is gradual deterioration and atrophy of some portions of the brain which are responsible for functioning of vital internal functions of the body like the blood pressure, digestion, and movement.

Autonomic failure was made evident by physical examiration as well as laboratory tests. These functions include the autonomic or involuntary nervous system which controls blood pressure, heart rate, and bladder function and the motor system which controls balance and muscle movement. Ed disturb of speech is reported by other authors 9.

All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License.

There is no specific treatment to MSA until the present, only symptomatic interventions